CLINICAL-FEATURES AND HISTORY OF THE DESTRUCTIVE LUNG-DISEASE ASSOCIATED WITH ALPHA-1-ANTITRYPSIN DEFICIENCY OF ADULTS WITH PULMONARY SYMPTOMS

被引:241
作者
BRANTLY, ML
PAUL, LD
MILLER, BH
FALK, RT
WU, M
CRYSTAL, RG
机构
[1] NCI, CTR CLIN, DEPT DIAGNOST RADIOL, BETHESDA, MD 20205 USA
[2] NCI, ENVIRONM EPIDEMIOL BRANCH, POPULAT STUDIES SECT, BETHESDA, MD 20205 USA
[3] NHLBI, DIV EPIDEMIOL & CLIN APPLICAT, BETHESDA, MD 20892 USA
来源
AMERICAN REVIEW OF RESPIRATORY DISEASE | 1988年 / 138卷 / 02期
关键词
D O I
10.1164/ajrccm/138.2.327
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:327 / 336
页数:10
相关论文
共 72 条
[31]  
GADEK JE, 1980, CLIN RES PROC, V16, P27
[32]   ALPHA1-ANTITRYPSIN DEFICIENCY - THE RADIOLOGICAL FEATURES OF PULMONARY-EMPHYSEMA IN SUBJECTS OF PI-TYPE-Z AND PI-TYPE-SZ - A SURVEY BY THE BRITISH-THORACIC-ASSOCIATION [J].
GISHEN, P ;
SAUNDERS, AJS ;
TOBIN, MJ ;
HUTCHISON, DCS .
CLINICAL RADIOLOGY, 1982, 33 (04) :371-377
[33]   PATTERN OF LUNG DISEASE ASSOCIATED WITH ALPHA1 ANTITRYPSIN DEFICIENCY [J].
GUENTER, CA ;
WELCH, MH ;
RUSSELL, TR ;
HYDE, RM ;
HAMMARSTEN, JF .
ARCHIVES OF INTERNAL MEDICINE, 1968, 122 (03) :254-+
[34]  
HEPPER NGG, 1978, MAYO CLIN PROC, V53, P166
[35]  
HUBBARD R C, 1985, American Review of Respiratory Disease, V131, pA371
[36]  
HUNNINGHAKE GW, 1983, AM REV RESPIR DIS, V128, P833
[37]  
HUTCHISON DCS, 1980, CLIN RES PROC, V16, P315
[38]   ALPHA-1 ANTI-TRYPSIN DEFICIENCY - CLINICAL AND PHYSIOLOGICAL FEATURES IN HETEROZYGOTES OF PI-TYPE-SZ - A SURVEY BY THE BRITISH-THORACIC-ASSOCIATION [J].
HUTCHISON, DCS ;
TOBIN, MJ ;
COOK, PJL .
BRITISH JOURNAL OF DISEASES OF THE CHEST, 1983, 77 (01) :28-34
[39]  
JANOFF A, 1977, AM REV RESPIR DIS, V115, P461
[40]  
JANUS ED, 1985, LANCET, V1, P152