CLINICAL-FEATURES AND HISTORY OF THE DESTRUCTIVE LUNG-DISEASE ASSOCIATED WITH ALPHA-1-ANTITRYPSIN DEFICIENCY OF ADULTS WITH PULMONARY SYMPTOMS

被引:241
作者
BRANTLY, ML
PAUL, LD
MILLER, BH
FALK, RT
WU, M
CRYSTAL, RG
机构
[1] NCI, CTR CLIN, DEPT DIAGNOST RADIOL, BETHESDA, MD 20205 USA
[2] NCI, ENVIRONM EPIDEMIOL BRANCH, POPULAT STUDIES SECT, BETHESDA, MD 20205 USA
[3] NHLBI, DIV EPIDEMIOL & CLIN APPLICAT, BETHESDA, MD 20892 USA
来源
AMERICAN REVIEW OF RESPIRATORY DISEASE | 1988年 / 138卷 / 02期
关键词
D O I
10.1164/ajrccm/138.2.327
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:327 / 336
页数:10
相关论文
共 72 条
[21]  
ERIKSSON S, 1972, PULMONARY EMPHYSEMA, P7
[22]   PREVALENCE OF ALPHA 1-ANTITRYPSIN PI-TYPES AMONG NEWBORN-INFANTS OF DIFFERENT ETHNIC BACKGROUNDS [J].
EVANS, HE ;
BOGNACKI, NS ;
PERROTT, LM ;
GLASS, L .
JOURNAL OF PEDIATRICS, 1977, 90 (04) :621-624
[23]  
Fagerhol M K, 1981, Adv Hum Genet, V11, P1
[24]   SERUM PI TYPES IN PATIENTS WITH PULMONARY DISEASES [J].
FAGERHOL, MK ;
HAUGE, HE .
ACTA ALLERGOLOGICA, 1969, 24 (02) :107-&
[25]  
FAGERHOL MK, 1968, ACTA PATHOL MIC SC, V72, P601
[26]  
FALLAT RJ, 1973, J NUCL MED, V14, P5
[27]  
FISCH C, 1984, HEART DISEASE TXB CA, P207
[28]   SMALL AIRWAYS IN IDIOPATHIC PULMONARY FIBROSIS - COMPARISON OF MORPHOLOGIC AND PHYSIOLOGIC OBSERVATIONS [J].
FULMER, JD ;
ROBERTS, WC ;
GAL, ERV ;
CRYSTAL, RG .
JOURNAL OF CLINICAL INVESTIGATION, 1977, 60 (03) :595-610
[29]  
Gadek J., 1982, METABOLIC BASIS INHE, P1450
[30]   ANTI-ELASTASES OF THE HUMAN ALVEOLAR STRUCTURES - IMPLICATIONS FOR THE PROTEASE-ANTIPROTEASE THEORY OF EMPHYSEMA [J].
GADEK, JE ;
FELLS, GA ;
ZIMMERMAN, RL ;
RENNARD, SI ;
CRYSTAL, RG .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (04) :889-898