共 26 条
MOLECULAR-BASIS FOR THE DEFICIENCY OF COMPLEMENT-1 INHIBITOR IN TYPE-I HEREDITARY ANGIONEUROTIC-EDEMA
被引:65
作者:

CICARDI, M
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR, DIV IMMUNOL, 300 LONGWOOD AVE, BOSTON, MA 02115 USA

IGARASHI, T
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR, DIV IMMUNOL, 300 LONGWOOD AVE, BOSTON, MA 02115 USA

ROSEN, FS
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR, DIV IMMUNOL, 300 LONGWOOD AVE, BOSTON, MA 02115 USA

DAVIS, AE
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR, DIV IMMUNOL, 300 LONGWOOD AVE, BOSTON, MA 02115 USA
机构:
[1] CHILDRENS HOSP MED CTR, DIV IMMUNOL, 300 LONGWOOD AVE, BOSTON, MA 02115 USA
[2] CHILDRENS HOSP MED CTR, DIV NEPHROL, BOSTON, MA 02115 USA
[3] HARVARD UNIV, SCH MED, DEPT PEDIAT, BOSTON, MA 02115 USA
关键词:
D O I:
10.1172/JCI112873
中图分类号:
R-3 [医学研究方法];
R3 [基础医学];
学科分类号:
1001 ;
摘要:
引用
收藏
页码:698 / 702
页数:5
相关论文
共 26 条
[1]
BIOSYNTHESIS INVITRO OF COMPLEMENT SUBCOMPONENT-C1Q, SUBCOMPONENT-C1S AND SUBCOMPONENT-C1 INHIBITOR BY RESTING AND STIMULATED HUMAN-MONOCYTES
[J].
BENSA, JC
;
REBOUL, A
;
COLOMB, MG
.
BIOCHEMICAL JOURNAL,
1983, 216 (02)
:385-392

BENSA, JC
论文数: 0 引用数: 0
h-index: 0
机构: DEPT RECH FONDEMENTALE GRENOBLE,DEPT IMMUNOCHIM SYST COMPLEMENTAIRE,GRENOBLE,FRANCE

REBOUL, A
论文数: 0 引用数: 0
h-index: 0
机构: DEPT RECH FONDEMENTALE GRENOBLE,DEPT IMMUNOCHIM SYST COMPLEMENTAIRE,GRENOBLE,FRANCE

COLOMB, MG
论文数: 0 引用数: 0
h-index: 0
机构: DEPT RECH FONDEMENTALE GRENOBLE,DEPT IMMUNOCHIM SYST COMPLEMENTAIRE,GRENOBLE,FRANCE
[2]
DELETION OF COMPLEMENT C-4 AND STEROID 21-HYDROXYLASE GENES IN THE HLA CLASS-III REGION
[J].
CARROLL, MC
;
PALSDOTTIR, A
;
BELT, KT
;
PORTER, RR
.
EMBO JOURNAL,
1985, 4 (10)
:2547-2552

CARROLL, MC
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND

PALSDOTTIR, A
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND

BELT, KT
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND UNIV OXFORD,DEPT BIOCHEM,OXFORD OX1 3QU,ENGLAND

论文数: 引用数:
h-index:
机构:
[3]
ISOLATION OF BIOLOGICALLY-ACTIVE RIBONUCLEIC-ACID FROM SOURCES ENRICHED IN RIBONUCLEASE
[J].
CHIRGWIN, JM
;
PRZYBYLA, AE
;
MACDONALD, RJ
;
RUTTER, WJ
.
BIOCHEMISTRY,
1979, 18 (24)
:5294-5299

CHIRGWIN, JM
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143 UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143

PRZYBYLA, AE
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143 UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143

MACDONALD, RJ
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143 UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143

RUTTER, WJ
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143 UNIV CALIF SAN FRANCISCO,DEPT BIOCHEM & BIOPHYS,SAN FRANCISCO,CA 94143
[4]
HEREDITARY ANGIOEDEMA - AN APPRAISAL OF 104 CASES
[J].
CICARDI, M
;
BERGAMASCHINI, L
;
MARASINI, B
;
BOCCASSINI, G
;
TUCCI, A
;
AGOSTONI, A
.
AMERICAN JOURNAL OF THE MEDICAL SCIENCES,
1982, 284 (01)
:2-9

CICARDI, M
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY

BERGAMASCHINI, L
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY

MARASINI, B
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY

BOCCASSINI, G
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY

TUCCI, A
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY

AGOSTONI, A
论文数: 0 引用数: 0
h-index: 0
机构:
UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY UNIV MILAN,DEPT CLIN MED,I-20133 MILAN,ITALY
[5]
THE MOLECULAR-BASIS FOR GENETIC DEFICIENCY OF THE 2ND COMPONENT OF HUMAN-COMPLEMENT
[J].
COLE, FS
;
WHITEHEAD, AS
;
AUERBACH, HS
;
LINT, T
;
ZEITZ, HJ
;
KILBRIDGE, P
;
COLTEN, HR
.
NEW ENGLAND JOURNAL OF MEDICINE,
1985, 313 (01)
:11-16

COLE, FS
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

WHITEHEAD, AS
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

AUERBACH, HS
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

LINT, T
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

ZEITZ, HJ
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

KILBRIDGE, P
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115

COLTEN, HR
论文数: 0 引用数: 0
h-index: 0
机构: BRIGHAM & WOMENS HOSP,JOINT PROGRAM NEONATOL,BOSTON,MA 02115
[6]
HUMAN INHIBITOR OF THE 1ST COMPONENT OF COMPLEMENT, C1 - CHARACTERIZATION OF CDNA CLONES AND LOCALIZATION OF THE GENE TO CHROMOSOME-11
[J].
DAVIS, AE
;
WHITEHEAD, AS
;
HARRISON, RA
;
DAUPHINAIS, A
;
BRUNS, GAP
;
CICARDI, M
;
ROSEN, FS
.
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA,
1986, 83 (10)
:3161-3165

DAVIS, AE
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

WHITEHEAD, AS
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

HARRISON, RA
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

DAUPHINAIS, A
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

BRUNS, GAP
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

CICARDI, M
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115

ROSEN, FS
论文数: 0 引用数: 0
h-index: 0
机构: CHILDRENS HOSP MED CTR,DIV NEPHROL,BOSTON,MA 02115
[7]
A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE
[J].
DONALDSON, VH
;
EVANS, RR
.
AMERICAN JOURNAL OF MEDICINE,
1963, 35 (01)
:37-+

DONALDSON, VH
论文数: 0 引用数: 0
h-index: 0

EVANS, RR
论文数: 0 引用数: 0
h-index: 0
[8]
VARIABILITY IN PURIFIED DYSFUNCTIONAL C1-INHIBITOR PROTEINS FROM PATIENTS WITH HEREDITARY ANGIONEUROTIC-EDEMA - FUNCTIONAL AND ANALYTICAL GEL STUDIES
[J].
DONALDSON, VH
;
HARRISON, RA
;
ROSEN, FS
;
BING, DH
;
KINDNESS, G
;
CANAR, J
;
WAGNER, CJ
;
AWAD, S
.
JOURNAL OF CLINICAL INVESTIGATION,
1985, 75 (01)
:124-132

DONALDSON, VH
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

HARRISON, RA
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

ROSEN, FS
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

BING, DH
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

KINDNESS, G
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

CANAR, J
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

WAGNER, CJ
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

AWAD, S
论文数: 0 引用数: 0
h-index: 0
机构: UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
[9]
SYNTHESIS OF 2ND COMPONENT OF COMPLEMENT BY LONG-TERM PRIMARY CULTURES OF HUMAN MONOCYTES
[J].
EINSTEIN, LP
;
SCHNEEBERGER, EE
;
COLTEN, HR
.
JOURNAL OF EXPERIMENTAL MEDICINE,
1976, 143 (01)
:114-126

EINSTEIN, LP
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV,MED SCH,DEPT PATHOL,BOSTON,MA 02115

SCHNEEBERGER, EE
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV,MED SCH,DEPT PATHOL,BOSTON,MA 02115

COLTEN, HR
论文数: 0 引用数: 0
h-index: 0
机构: HARVARD UNIV,MED SCH,DEPT PATHOL,BOSTON,MA 02115
[10]
RESPONSE OF VARIANT HEREDITARY ANGIOEDEMA PHENOTYPES TO DANAZOL THERAPY - GENETIC-IMPLICATIONS
[J].
GADEK, JE
;
HOSEA, SW
;
GELFAND, JA
;
FRANK, MM
.
JOURNAL OF CLINICAL INVESTIGATION,
1979, 64 (01)
:280-286

GADEK, JE
论文数: 0 引用数: 0
h-index: 0
机构:
NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA

HOSEA, SW
论文数: 0 引用数: 0
h-index: 0
机构:
NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA

GELFAND, JA
论文数: 0 引用数: 0
h-index: 0
机构:
NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA

FRANK, MM
论文数: 0 引用数: 0
h-index: 0
机构:
NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA NIAID, CLIN INVEST LAB, BETHESDA, MD 20014 USA