VARIABILITY IN PURIFIED DYSFUNCTIONAL C1-INHIBITOR PROTEINS FROM PATIENTS WITH HEREDITARY ANGIONEUROTIC-EDEMA - FUNCTIONAL AND ANALYTICAL GEL STUDIES

被引：55

作者：

DONALDSON, VH

HARRISON, RA

ROSEN, FS

BING, DH

KINDNESS, G

CANAR, J

WAGNER, CJ

AWAD, S

机构：

[1] UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229

[2] UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT MED,CINCINNATI,OH 45229

[3] MRC CTR,MECH TUMOUR IMMUN UNIT,CAMBRIDGE CB2 2QH,ENGLAND

[4] HARVARD UNIV,SCH MED,DEPT PEDIAT,BOSTON,MA 02115

[5] BETH ISRAEL HOSP,BOSTON,MA 02215

[6] COLL TECHNOL DUNDEE,DEPT MOLEC,DUNDEE,SCOTLAND

[7] COLL TECHNOL DUNDEE,DEPT LIFE SCI,DUNDEE,SCOTLAND

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1985年 / 75卷 / 01期

关键词：

D O I：

10.1172/JCI111664

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：124 / 132

页数：9

共 33 条

[1]

ASSIMEH SN, 1974, J IMMUNOL, V113, P225

[2]

BING DH, 1971, J IMMUNOL, V107, P1243

[3] HEREDITARY ANGIO-OEDEMA TREATED WITH E-AMINOCAPROIC ACID [J].

CHAMPION, RH ;

LACHMANN, PJ .

BRITISH JOURNAL OF DERMATOLOGY, 1969, 81 (10) :763-&

[4] PLASMINOGEN - PURIFICATION FROM HUMAN PLASMA BY AFFINITY CHROMATOGRAPHY [J].

DEUTSCH, DG ;

MERTZ, ET .

SCIENCE, 1970, 170 (3962) :1095-+

[5] A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE [J].

DONALDSON, VH ;

EVANS, RR .

AMERICAN JOURNAL OF MEDICINE, 1963, 35 (01) :37-+

[6]

DONALDSON VH, 1982, BLOOD, V60, P121

[7]

Finkenstadt W. R., 1965, J BIOL CHEM, V240, P962

[8]

GIGLI I, 1970, J IMMUNOL, V104, P574

[9]

HADJIYANNAKI K, 1971, Clinical Allergy, V1, P221, DOI 10.1111/j.1365-2222.1971.tb03021.x

[10]

Harpel P C, 1976, Prog Hemost Thromb, V3, P145

← 1 2 3 4 →