LEUKOCYTES FROM 4 PATIENTS WITH COMPLETE OR PARTIAL LEU-CAM DEFICIENCY CONTAIN THE COMMON BETA-SUBUNIT PRECURSOR AND BETA-SUBUNIT MESSENGER-RNA

被引:68
作者
DANA, N
CLAYTON, LK
TENNEN, DG
PIERCE, MW
LACHMANN, PJ
LAW, SA
ARNAOUT, MA
机构
[1] CHILDRENS HOSP MED CTR,DIV RENAL,BOSTON,MA 02115
[2] CHILDRENS HOSP MED CTR,DIV IMMUNOL,BOSTON,MA 02115
[3] BETH ISRAEL HOSP,DIV HEMATOL ONCOL,BOSTON,MA 02215
[4] MASSACHUSETTS GEN HOSP,HOWARD HUGHES MED INST,BOSTON,MA 02114
[5] MASSACHUSETTS GEN HOSP,DIV ENDOCRINOL,BOSTON,MA 02114
[6] HARVARD UNIV,SCH MED,BOSTON,MA 02115
[7] MRC,MECHANISMS TUMOR IMMUN UNIT,CAMBRIDGE CB2 2QH,ENGLAND
[8] UNIV OXFORD,MRC,IMMUNOCHEM UNIT,OXFORD,ENGLAND
关键词
D O I
10.1172/JCI112868
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1010 / 1015
页数:6
相关论文
共 30 条
[1]   ABNORMALITIES OF POLYMORPHONUCLEAR LEUKOCYTE FUNCTION ASSOCIATED WITH A HERITABLE DEFICIENCY OF HIGH MOLECULAR-WEIGHT SURFACE GLYCOPROTEINS (GP138) - COMMON RELATIONSHIP TO DIMINISHED CELL ADHERENCE [J].
ANDERSON, DC ;
SCHMALSTIEG, FC ;
ARNAOUT, MA ;
KOHL, S ;
TOSI, MF ;
DANA, N ;
BUFFONE, GJ ;
HUGHES, BJ ;
BRINKLEY, BR ;
DICKEY, WD ;
ABRAMSON, JS ;
SPRINGER, T ;
BOXER, LA ;
HOLLERS, JM ;
SMITH, CW .
JOURNAL OF CLINICAL INVESTIGATION, 1984, 74 (02) :536-551
[2]   DEFICIENCY OF A LEUKOCYTE SURFACE GLYCOPROTEIN (LFA-1) IN 2 PATIENTS WITH MO1 DEFICIENCY - EFFECTS OF CELL ACTIVATION ON MO1 LFA-1 SURFACE EXPRESSION IN NORMAL AND DEFICIENT LEUKOCYTES [J].
ARNAOUT, MA ;
SPITS, H ;
TERHORST, C ;
PITT, J ;
TODD, RF .
JOURNAL OF CLINICAL INVESTIGATION, 1984, 74 (04) :1291-1300
[3]  
ARNAOUT MA, 1985, FED PROC, V44, P2664
[4]   BIOSYNTHESIS OF THE HUMAN C3B/C4B RECEPTOR DURING DIFFERENTIATION OF THE HL-60 CELL-LINE - IDENTIFICATION AND CHARACTERIZATION OF A PRECURSOR MOLECULE [J].
ATKINSON, JP ;
JONES, EA .
JOURNAL OF CLINICAL INVESTIGATION, 1984, 74 (05) :1649-1657
[6]   ISOLATION OF BIOLOGICALLY-ACTIVE RIBONUCLEIC-ACID FROM SOURCES ENRICHED IN RIBONUCLEASE [J].
CHIRGWIN, JM ;
PRZYBYLA, AE ;
MACDONALD, RJ ;
RUTTER, WJ .
BIOCHEMISTRY, 1979, 18 (24) :5294-5299
[7]   NUMBER AND EVOLUTIONARY CONSERVATION OF ALPHA-TUBULIN AND BETA-TUBULIN AND CYTOPLASMIC BETA-ACTIN AND GAMMA-ACTIN GENES USING SPECIFIC CLONED CDNA PROBES [J].
CLEVELAND, DW ;
LOPATA, MA ;
MACDONALD, RJ ;
COWAN, NJ ;
RUTTER, WJ ;
KIRSCHNER, MW .
CELL, 1980, 20 (01) :95-105
[8]   AN INHERITED ABNORMALITY OF NEUTROPHIL ADHESION - ITS GENETIC TRANSMISSION AND ITS ASSOCIATION WITH A MISSING PROTEIN [J].
CROWLEY, CA ;
CURNUTTE, JT ;
ROSIN, RE ;
ANDRESCHWARTZ, J ;
GALLIN, JI ;
KLEMPNER, M ;
SNYDERMAN, R ;
SOUTHWICK, FS ;
STOSSEL, TP ;
BABIOR, BM .
NEW ENGLAND JOURNAL OF MEDICINE, 1980, 302 (21) :1163-1168
[9]   EARLY AND LATE FUNCTIONS ASSOCIATED WITH THE GOLGI-APPARATUS RESIDE IN DISTINCT COMPARTMENTS [J].
DUNPHY, WG ;
FRIES, E ;
URBANI, LJ ;
ROTHMAN, JE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1981, 78 (12) :7453-7457
[10]  
FEINBERG AP, 1984, ANAL BIOCHEM, V137, P266