CLINICAL AND BIOCHEMICAL CORRELATIONS IN MITOCHONDRIAL MYOPATHIES TREATED WITH COENZYME-Q10

被引:97
作者
BRESOLIN, N
BET, L
BINDA, A
MOGGIO, M
COMI, G
NADOR, F
FERRANTE, C
CARENZI, A
SCARLATO, G
机构
[1] ZAMBON PHARMACEUT CO,RES LAB,MILANO,ITALY
[2] OSPED MAGGIORE POLICLIN,DEPT CARDIOL,MILANO,ITALY
关键词
D O I
10.1212/WNL.38.6.892
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:892 / 899
页数:8
相关论文
共 45 条
[11]  
DELONG GR, 1982, PEDIATR RES, V16, P333
[12]   PROGRESSIVE OPHTHALMOPLEGIA, GLYCOGEN-STORAGE, AND ABNORMAL MITOCHONDRIA [J].
DIMAURO, S ;
SCHOTLAND, DL ;
BONILLA, E ;
LEE, CP ;
GAMBETTI, P ;
ROWLAND, LP .
ARCHIVES OF NEUROLOGY, 1973, 29 (03) :170-179
[13]   MITOCHONDRIAL MYOPATHIES [J].
DIMAURO, S ;
BONILLA, E ;
ZEVIANI, M ;
NAKAGAWA, M ;
DEVIVO, DC .
ANNALS OF NEUROLOGY, 1985, 17 (06) :521-538
[14]  
DRACHMAN DA, 1975, HDB CLIN NEUROLOGY, V22, P221
[15]   RESPONSE OF GENETICALLY DYSTROPHIC MICE TO THERAPY WITH HEXAHYDROCOENZYME Q4 [J].
FARLEY, TM ;
SCHOLLER, J ;
FOLKERS, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1966, 24 (03) :299-+
[16]   EFFECT OF COENZYME-Q ON SERUM LEVELS OF CREATINE-PHOSPHOKINASE IN PRECLINICAL MUSCULAR-DYSTROPHY [J].
FOLKERS, K ;
NAKAMURA, R ;
LITTARRU, GP ;
ZELLWEGE.H ;
BRUNKHOR.JB ;
WILLIAMS, CW ;
LANGSTON, JH .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1974, 71 (05) :2098-2102
[17]   BIOCHEMICAL RATIONALE AND THE CARDIAC RESPONSE OF PATIENTS WITH MUSCLE DISEASE TO THERAPY WITH COENZYME-Q10 [J].
FOLKERS, K ;
WOLANIUK, J ;
SIMONSEN, R ;
MORISHITA, M ;
VADHANAVIKIT, S .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1985, 82 (13) :4513-4516
[18]   MITOCHONDRIAL ABNORMALITIES IN PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA [J].
HYMAN, BN ;
PATTEN, BM ;
DODSON, RF .
AMERICAN JOURNAL OF OPHTHALMOLOGY, 1977, 83 (03) :362-&
[19]  
IZUMI K, 1980, JPN J CLIN EXP MED, V57, P1
[20]   A PARTIAL DEFICIENCY OF CYTOCHROME-C OXIDASE IN CHRONIC PROGRESSIVE EXTERNAL OPHTHALMOPLEGIA [J].
JOHNSON, MA ;
TURNBULL, DM ;
DICK, DJ ;
SHERRATT, HSA .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1983, 60 (01) :31-53