QUANTITATIVE ASPECTS OF PINOCYTOSIS AND INTRACELLULAR FATE OF N-ACETYL-ALPHA-D-GLUCOSAMINIDASE IN SANFILIPPO-B FIBROBLASTS

被引：20

作者：

FIGURA, KV ^{[1
]}

KRESSE, H ^{[1
]}

机构：

[1] UNIV MUNSTER,INST PHYSIOL CHEM,D-44 MUNSTER,WEST GERMANY

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1974年 / 53卷 / 01期

关键词：

D O I：

10.1172/JCI107563

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：85 / 90

页数：6

共 19 条

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[2]

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[3]

DEKABAN AS, 1972, PEDIATRICS, V50, P688

[4]

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[5]

ERICKSON RP, 1972, PEDIATRICS, V50, P693

[6] SANFILIPPO-B DISEASE - SERUM ASSAYS FOR DETECTION OF HOMOZYGOUS AND HETEROZYGOUS INDIVIDUALS IN THREE FAMILIES [J].

FIGURA, KV ;

LOGERING, M ;

MERSMANN, G ;

KRESSE, H .

JOURNAL OF PEDIATRICS, 1973, 83 (04) :607-611

[7]

FIGURA KV, 1972, BIOCHEM BIOPH RES CO, V48, P262

[8] DEFECT IN HURLER AND HUNTER SYNDROMES, .2. DEFICIENCY OF SPECIFIC FACTORS INVOLVED IN MUCOPOLYSACCHARIDE DEGRADATION [J].

FRATANTO.JC ;

HALL, CW ;

NEUFELD, EF .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1969, 64 (01) :360-&

[9] HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES [J].

HICKMAN, S ;

NEUFELD, EF .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 49 (04) :992-&

[10]

JACQUES PJ, 1969, LYSOSOMES BIOLOGY PA, V2

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