ALPHA-1-ANTITRYPSIN - MOLECULAR PATHOLOGY, LEUKOCYTES, AND TISSUE-DAMAGE

被引:252
作者
CARRELL, RW
机构
关键词
D O I
10.1172/JCI112731
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1427 / 1431
页数:5
相关论文
共 68 条
[1]   REGULATION OF ALPHA-1 PROTEINASE-INHIBITOR FUNCTION BY RABBIT ALVEOLAR MACROPHAGES - EVIDENCE FOR PROTEOLYTIC RATHER THAN OXIDATIVE INACTIVATION [J].
BANDA, MJ ;
CLARK, EJ ;
WERB, Z .
JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (06) :1758-1762
[2]   HUMAN Z-ALPHA-1-ANTITRYPSIN ACCUMULATES INTRACELLULARLY AND STIMULATES LYSOSOMAL ACTIVITY WHEN SYNTHESIZED IN THE XENOPUS OOCYTE [J].
BATHURST, IC ;
ERRINGTON, DM ;
FOREMAN, RC ;
JUDAH, JD ;
CARRELL, RW .
FEBS LETTERS, 1985, 183 (02) :304-308
[3]   TRANSLATION AND PROCESSING OF NORMAL (PIMM) AND ABNORMAL (PIZZ) HUMAN ALPHA-1-ANTITRYPSIN [J].
BATHURST, IC ;
STENFLO, J ;
ERRINGTON, DM ;
CARRELL, RW .
FEBS LETTERS, 1983, 153 (02) :270-274
[4]   STRUCTURAL AND FUNCTIONAL-CHARACTERIZATION OF THE ABNORMAL Z-ALPHA1-ANTITRYPSIN ISOLATED FROM HUMAN-LIVER [J].
BATHURST, IC ;
TRAVIS, J ;
GEORGE, PM ;
CARRELL, RW .
FEBS LETTERS, 1984, 177 (02) :179-183
[5]   LIVER IN ALPHA-1-ANTITRYPSIN DEFICIENCY - MORPHOLOGIC OBSERVATIONS AND INVITRO SYNTHESIS OF ALPHA-1-ANTITRYPSIN [J].
BHAN, AK ;
GRAND, RJ ;
COLTEN, HR ;
ALPER, CA .
PEDIATRIC RESEARCH, 1976, 10 (01) :35-40
[6]  
Boswell D. R., 1986, REC ADV CLIN IMMUNOL, V4, P1
[7]  
BROWER MS, 1982, J BIOL CHEM, V257, P9849
[8]  
CARLSON J, 1984, THESIS U LUND SWEDEN
[9]  
CARP H, 1978, AM REV RESPIR DIS, V118, P617
[10]   INVITRO SUPPRESSION OF SERUM ELASTASE-INHIBITORY CAPACITY BY REACTIVE OXYGEN SPECIES GENERATED BY PHAGOCYTOSING POLYMORPHONUCLEAR LEUKOCYTES [J].
CARP, H ;
JANOFF, A .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 63 (04) :793-797