GUIDELINES FOR THE APPROACH TO THE PATIENT WITH SEVERE HEREDITARY ALPHA-1-ANTITRYPSIN DEFICIENCY

被引:83
作者
BUIST, AS
BURROWS, B
COHEN, A
CRYSTAL, RG
FALLAT, RJ
GADEK, JE
TURINO, GM
机构
[1] UNIV ARIZONA,DIV RESP SCI,TUCSON,AZ 85724
[2] UNIV TEXAS,CTR HLTH,TYLER,TX 75710
[3] NHLBI,PULM BRANCH,BETHESDA,MD 20892
[4] PACIFIC PRESBYTERIAN MED CTR,DEPT PULM MED,SAN FRANCISCO,CA 94120
[5] OHIO STATE UNIV,DIV PULM & CRIT CARE,COLUMBUS,OH 43210
[6] ST LUKES ROOSEVELT HOSP,NEW YORK,NY 10019
来源
AMERICAN REVIEW OF RESPIRATORY DISEASE | 1989年 / 140卷 / 05期
关键词
D O I
10.1164/ajrccm/140.5.1494
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
引用
收藏
页码:1494 / 1497
页数:4
相关论文
共 16 条
[1]  
BRANTLY M, 1988, AM J MED, V84, P13
[2]   THE ALPHA-1-ANTITRYPSIN GENE AND ITS MUTATIONS - CLINICAL CONSEQUENCES AND STRATEGIES FOR THERAPY [J].
CRYSTAL, RG ;
BRANTLY, ML ;
HUBBARD, RC ;
CURIEL, DT ;
STATES, DJ ;
HOLMES, MD .
CHEST, 1989, 95 (01) :196-208
[3]  
ERIKKSON S, 1986, NEW ENGL J MED, V314, P734
[5]  
Fagerhol M K, 1981, Adv Hum Genet, V11, P1
[6]  
HUBBARD RC, 1988, AM J MED, V84, P52
[7]   BIOCHEMICAL EFFICACY AND SAFETY OF MONTHLY AUGMENTATION THERAPY FOR ALPHA-1-ANTITRYPSIN DEFICIENCY [J].
HUBBARD, RC ;
SELLERS, S ;
CZERSKI, D ;
STEPHENS, L ;
CRYSTAL, RG .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1988, 260 (09) :1259-1264
[8]  
HUTCHISON DCS, 1988, AM J MED, V84, P3
[9]  
JANOFF A, 1985, AM REV RESPIR DIS, V132, P417
[10]   NATURAL-HISTORY AND LIFE EXPECTANCY IN SEVERE ALPHA1-ANTITRYPSIN DEFICIENCY, PIZ [J].
LARSSON, C .
ACTA MEDICA SCANDINAVICA, 1978, 204 (05) :345-351