RAPID POSTSYNTHETIC DESTRUCTION OF UNSTABLE HEMOGLOBIN BUSHWICK

被引:44
作者
RIEDER, RF
WOLF, DJ
CLEGG, JB
LEE, SL
机构
[1] SUNY, DOWNSTATE MED CTR, DEPT MED, BROOKLYN, NY 11203 USA
[2] UNIV OXFORD, RADCLIFFE INFIRM, NUFFIELD DEPT CLIN MED, OXFORD OX2 6HE, ENGLAND
[3] JEWISH HOSP & MED CTR, DEPT MED, BROOKLYN, NY 11328 USA
关键词
D O I
10.1038/254725a0
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:725 / 727
页数:3
相关论文
共 26 条
[1]   ABNORMAL HUMAN HAEMOGLOBINS - SEPARATION AND CHARACTERIZATION OF ALPHA AND BETA CHAINS BY CHROMATOGRAPHY AND DETERMINATION OF 2 NEW VARIANTS HB CHESAPEAKE AND HB J (BANGKOK) [J].
CLEGG, JB ;
NAUGHTON, MA ;
WEATHERA.DJ .
JOURNAL OF MOLECULAR BIOLOGY, 1966, 19 (01) :91-&
[2]  
COHENSOLAL M, 1973, BIOCHIM BIOPHYS ACTA, V295, P67
[3]   MOLECULAR DEFECT OF FERRARA BETA-THALASSEMIA [J].
CONCONI, F ;
SENNO, LD .
ANNALS OF THE NEW YORK ACADEMY OF SCIENCES, 1974, 232 (MAY24) :54-64
[4]  
DAYHOFF MO, 1972, ATLAS PROTEIN SEQUEN, V5
[5]   PROTEIN SYNTHESIS IN CELL-FREE SYSTEMS FROM RETICULOCYTES OF THALASSAEMIC PATIENTS [J].
FUHR, J ;
NATTA, C ;
MARKS, PA ;
BANK, A .
NATURE, 1969, 224 (5226) :1305-&
[6]  
HOLLAN SR, 1972, NATURE, V235, P47, DOI 10.1038/235047a0
[7]   NEW UNSTABLE HAEMOGLOBIN BORAS - BETA88 (F4) LEUCINE-]ARGININE [J].
HOLLENDER, A ;
LORKIN, PA ;
LEHMANN, H ;
SVENSSON, B .
NATURE, 1969, 222 (5197) :953-+
[8]   SYNTHESIS OF HEMOGLOBIN ABRAHAM LINCOLN (BETA 32 LEU-]PRO) [J].
HONIG, GR ;
MASON, RG ;
VIDA, LN ;
SHAMSUDDIN, M .
BLOOD, 1974, 43 (05) :657-664
[9]   HEMOGLOBIN LINCOLN,A, BETA-32(B14)LEUCINE-]PROLINE (B14) - UNSTABLE VARIANT PRODUCING SEVERE HEMOLYTIC DISEASE [J].
HONIG, GR ;
GREEN, D ;
SHAMSUDDIN, M ;
VIDA, LN ;
MASON, RG ;
GNARRA, DJ ;
MAURER, HS .
JOURNAL OF CLINICAL INVESTIGATION, 1973, 52 (07) :1746-1755
[10]  
HUEHNS ER, 1971, B SOC CHIM BIOL, V52, P1131