A PRION PROTEIN MISSENSE VARIANT IS INTEGRATED IN KURU PLAQUE CORES IN PATIENTS WITH GERSTMANN-STRAUSSLER SYNDROME

被引:41
作者
KITAMOTO, T
YAMAGUCHI, K
DOHURA, K
TATEISHI, J
机构
[1] KYOWA HAKKO KOGYO CO LTD,TOKYO RES LABS,TOKYO,JAPAN
[2] KYUSHU UNIV,DEPT NEUROPATHOL,FUKUOKA 812,JAPAN
关键词
D O I
10.1212/WNL.41.2_Part_1.306
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
收藏
页码:306 / 310
页数:5
相关论文
共 35 条
[1]   ANTIBODIES TO A SCRAPIE PRION PROTEIN [J].
BENDHEIM, PE ;
BARRY, RA ;
DEARMOND, SJ ;
STITES, DP ;
PRUSINER, SB .
NATURE, 1984, 310 (5976) :418-421
[2]   CREUTZFELDT-JAKOB DISEASE PRION PROTEINS IN HUMAN BRAINS [J].
BOCKMAN, JM ;
KINGSBURY, DT ;
MCKINLEY, MP ;
BENDHEIM, PE ;
PRUSINER, SB .
NEW ENGLAND JOURNAL OF MEDICINE, 1985, 312 (02) :73-78
[3]   DIAGNOSIS OF CREUTZFELDT-JAKOB DISEASE BY WESTERN-BLOT IDENTIFICATION OF MARKER PROTEIN IN HUMAN-BRAIN TISSUE [J].
BROWN, P ;
COKERVANN, M ;
POMEROY, K ;
FRANKO, M ;
ASHER, DM ;
GIBBS, CJ ;
GAJDUSEK, DC .
NEW ENGLAND JOURNAL OF MEDICINE, 1986, 314 (09) :547-551
[4]   GENETICS AND POLYMORPHISM OF THE MOUSE PRION GENE-COMPLEX - CONTROL OF SCRAPIE INCUBATION-TIME [J].
CARLSON, GA ;
GOODMAN, PA ;
LOVETT, M ;
TAYLOR, BA ;
MARSHALL, ST ;
PETERSONTORCHIA, M ;
WESTAWAY, D ;
PRUSINER, SB .
MOLECULAR AND CELLULAR BIOLOGY, 1988, 8 (12) :5528-5540
[5]   PRION PROTEIN-BIOSYNTHESIS IN SCRAPIE-INFECTED AND UNINFECTED NEURO-BLASTOMA CELLS [J].
CAUGHEY, B ;
RACE, RE ;
ERNST, D ;
BUCHMEIER, MJ ;
CHESEBRO, B .
JOURNAL OF VIROLOGY, 1989, 63 (01) :175-181
[6]   PRO-]LEU CHANGE AT POSITION-102 OF PRION PROTEIN IS THE MOST COMMON BUT NOT THE SOLE MUTATION RELATED TO GERSTMANN-STRAUSSLER SYNDROME [J].
DOHURA, K ;
TATEISHI, J ;
SASAKI, H ;
KITAMOTO, T ;
SAKAKI, Y .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1989, 163 (02) :974-979
[7]   CREUTZFELDT-JAKOB DISEASE PATIENTS WITH CONGOPHILIC KURU PLAQUES HAVE THE MISSENSE VARIANT PRION PROTEIN COMMON TO GERSTMANN-STRAUSSLER SYNDROME [J].
DOHURA, K ;
TATEISHI, J ;
KITAMOTO, T ;
SASAKI, H ;
SAKAKI, Y .
ANNALS OF NEUROLOGY, 1990, 27 (02) :121-126
[8]   IMMUNOAFFINITY PURIFICATION AND NEUTRALIZATION OF SCRAPIE PRION INFECTIVITY [J].
GABIZON, R ;
MCKINLEY, MP ;
GROTH, D ;
PRUSINER, SB .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1988, 85 (18) :6617-6621
[9]   EXPERIMENTAL TRANSMISSION OF A KURU-LIKE SYNDROME TO CHIMPANZEES [J].
GAJDUSEK, DC ;
GIBBS, CJ ;
ALPERS, M .
NATURE, 1966, 209 (5025) :794-&
[10]   CREUTZFELDT-JAKOB DISEASE (SPONGIFORM ENCEPHALOPATHY) - TRANSMISSION TO CHIMPANZEE [J].
GIBBS, CJ ;
GAJDUSEK, DC ;
ASHER, DM ;
ALPERS, MP ;
BECK, E ;
DANIEL, PM ;
MATTHEWS, WB .
SCIENCE, 1968, 161 (3839) :388-&