ROLE OF GLYCOSIDICALLY BOUND MANNOSE IN ASSIMILATION OF BETA-GALACTOSIDASE BY GENERALIZED GANGLIOSIDOSIS FIBROBLASTS

被引:53
作者
HIEBER, V
DISTLER, J
MYEROWITZ, R
SCHMICKEL, RD
JOURDIAN, GW
机构
[1] UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT BIOL CHEM, ANN ARBOR, MI 48109 USA
[2] UNIV MICHIGAN, RACKHAM ARTHRITIS RES UNIT, DEPT PEDIAT, ANN ARBOR, MI 48109 USA
关键词
D O I
10.1016/0006-291X(76)90868-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:710 / 717
页数:8
相关论文
共 20 条
[2]  
BAHL OP, 1969, J BIOL CHEM, V244, P2970
[3]  
BATES FJ, 1942, C440 NBS CIRC, P519
[4]   PURIFICATION OF WHEAT-GERM AGGLUTININ USING AFFINITY CHROMATOGRAPHY ON CHITIN [J].
BLOCH, R ;
BURGER, MM .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 58 (01) :13-19
[5]  
CUATRECASAS P, 1970, J BIOL CHEM, V245, P3059
[6]  
Distler J, 1975, Birth Defects Orig Artic Ser, V11, P311
[7]  
DISTLER JJ, 1973, J BIOL CHEM, V248, P6772
[8]   RECOGNITION MARKER REQUIRED FOR UPTAKE OF A LYSOSOMAL ENZYME BY CULTURED FIBROBLASTS [J].
HICKMAN, S ;
SHAPIRO, LJ ;
NEUFELD, EF .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :55-61
[9]  
HIEBER V, 1976, FED PROC, V35, P1371
[10]  
LAGUNOFF D, 1973, LAB INVEST, V29, P449