HEME SYNTHETASE DEFICIENCY IN HUMAN PROTOPORPHYRIA - DEMONSTRATION OF DEFECT IN LIVER AND CULTURED SKIN FIBROBLASTS

被引：225

作者：

BONKOWSKY, HL

BLOOMER, JR

EBERT, PS

MAHONEY, MJ

机构：

[1] DARTMOUTH MED SCH,WHITE RIVER JUNCTION,VT 05001

[2] NCI,BETHESDA,MD 20014

[3] VET ADM HOSP,WHITE RIVER JUNCTION,VT 05001

[4] YALE UNIV,SCH MED,NEW HAVEN,CT 06510

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1975年 / 56卷 / 05期

关键词：

D O I：

10.1172/JCI108189

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：1139 / 1148

页数：10

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