METABOLISM OF SPHINGOMYELIN .2. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN NIEMANN-PICK DISEASE

被引：418

作者：

BRADY, RO

KANFER, JN

MOCK, MB

FREDRICKSON, DS

机构：

来源：

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA | 1966年 / 55卷 / 02期

关键词：

D O I：

10.1073/pnas.55.2.366

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：366 / +

页数：1

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KANFER, JN ;

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[3]

Chargaff E, 1939, J BIOL CHEM, V130, P503

[4] SPHINGOMYELIN SYNTHESIS IN NIEMANN-PICK DISEASE [J].

CROCKER, AC ;

MAYS, VB .

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[5] PHOSPHORYLCHOLINE IN RAT TISSUES [J].

DAWSON, RMC .

BIOCHEMICAL JOURNAL, 1955, 60 (1-4) :325-328

[6]

FREDRICKSON DC, 1966, METABOLIC BASIS INHE

[7]

KANFER JN, IN PRESS

[8] The nature of phosphatide and other lipoids of the brain and liver in Niemann Pick's disease. [J].

Klenk, E .

HOPPE-SEYLERS ZEITSCHRIFT FUR PHYSIOLOGISCHE CHEMIE, 1935, 235 :24-36

[9]

Klenk E., 1934, Z PHYSL CHEM, V229, P151

[10]

STANBURY JB, 1966, METABOLIC BASIS I ED

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