ABNORMAL TRANSBILAYER MOBILITY OF PHOSPHATIDYLCHOLINE IN HEREDITARY PYROPOIKILOCYTOSIS REFLECTS THE INCREASED HEAT SENSITIVITY OF THE MEMBRANE SKELETON

被引:27
作者
FRANCK, PFH
DENKAMP, JAFO
LUBIN, B
BERENDSEN, W
JOOSTEN, P
BRIET, E
VANDEENEN, LLM
ROELOFSEN, B
机构
[1] CHILDRENS HOSP MED CTR NO CALIF,DEPT HEMATOL ONCOL,OAKLAND,CA 94609
[2] LEIDEN STATE UNIV HOSP,DEPT HEMATOL,2333 AA LEIDEN,NETHERLANDS
[3] STATE UNIV UTRECHT,DEPT MOLEC CELL BIOL,3584 CH UTRECHT,NETHERLANDS
[4] CHILDRENS HOSP MED CTR NO CALIF,BRUCE LYON MEM RES LAB,OAKLAND,CA 94609
关键词
D O I
10.1016/0005-2736(85)90296-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:259 / 267
页数:9
相关论文
共 38 条
[1]   EFFECT OF TEMPERATURE ON THE RED-CELL MEMBRANE-PROTEIN AND ITS ANTIGENIC REACTIVITY [J].
BALLAS, SK ;
MIGUEL, O .
TRANSFUSION, 1981, 21 (05) :537-541
[2]   CALORIMETRIC STUDIES OF STRUCTURAL TRANSITIONS OF HUMAN ERYTHROCYTE-MEMBRANE - INVOLVEMENT OF SPECTRIN IN A-TRANSITION [J].
BRANDTS, JF ;
ERICKSON, L ;
LYSKO, K ;
SCHWARTZ, AT ;
TAVERNA, RD .
BIOCHEMISTRY, 1977, 16 (15) :3450-3454
[3]   QUANTITATIVE 2-DIMENSIONAL THIN-LAYER CHROMATOGRAPHY OF BLOOD PHOSPHOLIPIDS [J].
BROEKHUYSE, RM .
CLINICA CHIMICA ACTA, 1969, 23 (03) :457-+
[4]   EFFECT OF HEAT ON THE CIRCULAR-DICHROISM OF SPECTRIN IN HEREDITARY PYROPOIKILOCYTOSIS [J].
CHANG, K ;
WILLIAMSON, JR ;
ZARKOWSKY, HS .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (01) :326-328
[5]   ERYTHROCYTE-MEMBRANE LIPID REORGANIZATION DURING THE SICKLING PROCESS [J].
CHIU, D ;
LUBIN, B ;
SHOHET, SB .
BRITISH JOURNAL OF HAEMATOLOGY, 1979, 41 (02) :223-234
[6]  
COAKLEY WT, 1978, BIOCHIM BIOPHYS ACTA, V512, P318, DOI 10.1016/0005-2736(78)90256-0
[7]  
COHEN CM, 1983, SEMIN HEMATOL, V20, P141
[8]   ROLE OF MEMBRANE LIPIDS IN SURVIVAL OF RED CELLS IN HEREDITARY SPHEROCYTOSIS [J].
COOPER, RA ;
JANDL, JH .
JOURNAL OF CLINICAL INVESTIGATION, 1969, 48 (04) :736-&
[9]  
den Kamp J.A.F, 1979, ANNU REV BIOCHEM, V48, P47
[10]   UNCOUPLING OF THE MEMBRANE SKELETON FROM THE LIPID BILAYER - THE CAUSE OF ACCELERATED PHOSPHOLIPID FLIP-FLOP LEADING TO AN ENHANCED PROCOAGULANT ACTIVITY OF SICKLED CELLS [J].
FRANCK, PFH ;
BEVERS, EM ;
LUBIN, BH ;
COMFURIUS, P ;
CHIU, DTY ;
DENKAMP, JAFO ;
ZWAAL, RFA ;
VANDEENEN, LLM ;
ROELOFSEN, B .
JOURNAL OF CLINICAL INVESTIGATION, 1985, 75 (01) :183-190