APPARENT CATHEPSIN-B DEFICIENCY IN NEURONAL CEROID LIPOFUSCINOSIS CAN BE EXPLAINED BY PEROXIDE INHIBITION

被引：9

作者：

DAWSON, G

GLASER, P

机构：

[1] UNIV CHICAGO,DEPT BIOCHEM,CHICAGO,IL 60637

[2] UNIV CHICAGO,DEPT MOLEC BIOL,CHICAGO,IL 60637

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1987年 / 147卷 / 01期

关键词：

D O I：

10.1016/S0006-291X(87)80116-X

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：267 / 274

页数：8

共 22 条

[1] STUDIES IN BATTEN DISEASE .1. PEROXIDASE DEFICIENCY IN GRANULOCYTES [J].

ARMSTRONG, D ;

DIMMITT, S ;

VANWORMER, DE .

ARCHIVES OF NEUROLOGY, 1974, 30 (02) :144-152

[2]

Armstrong D, 1982, CEROID LIPOFUSCINOSI

[3]

BARRETT AJ, 1981, METHOD ENZYMOL, V80, P535

[4] SUBSTRATE-SPECIFICITY OF HUMAN ALPHA-L-FUCOSIDASE [J].

DAWSON, G ;

TSAY, G .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1977, 184 (01) :12-23

[5]

DAWSON G, 1982, CEROID LIPOFUSCINOSI, P229

[6]

DAWSON G, 1972, J BIOL CHEM, V244, P5944

[7] CONVERSION OF PROINSULIN TO INSULIN - INVOLVEMENT OF A 31,500 MOLECULAR-WEIGHT THIOL PROTEASE [J].

DOCHERTY, K ;

CARROLL, RJ ;

STEINER, DF .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15) :4613-4617

[8]

HEINRIKSON RL, 1977, J BIOL CHEM, V252, P4913

[9] N-ACETYLNEURAMINIC ACID ACCUMULATION IN A BUOYANT LYSOSOMAL FRACTION OF CULTURED FIBROBLASTS FROM PATIENTS WITH INFANTILE GENERALIZED N-ACETYLNEURAMINIC ACID STORAGE DISEASE [J].

HILDRETH, J ;

SACKS, L ;

HANCOCK, LW .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1986, 139 (02) :838-844

[10] INHIBITORS OF LYSOSOMAL-ENZYMES - ACCUMULATION OF LIPOFUSCIN-LIKE DENSE BODIES IN THE BRAIN [J].

IVY, GO ;

SCHOTTLER, F ;

WENZEL, J ;

BAUDRY, M ;

LYNCH, G .

SCIENCE, 1984, 226 (4677) :985-987

← 1 2 3 →