BIOCHEMICAL, IMMUNOLOGICAL, AND STRUCTURAL STUDIES ON A SPHINGOLIPID ACTIVATOR PROTEIN (SAP-1)

被引：47

作者：

INUI, K ^{[1
]}

WENGER, DA ^{[1
]}

机构：

[1] UNIV COLORADO,SCH MED,DEPT PEDIAT,DENVER,CO 80262

来源：

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS | 1984年 / 233卷 / 02期

关键词：

D O I：

10.1016/0003-9861(84)90479-X

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：556 / 564

页数：9

共 20 条

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[6]

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[7] IMMUNOLOGICAL EVIDENCE FOR DEFICIENCY IN AN ACTIVATOR PROTEIN FOR SULFATIDE SULFATASE IN A VARIANT FORM OF METACHROMATIC LEUKODYSTROPHY [J].

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PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (10) :3074-3077

[8] CONCENTRATIONS OF AN ACTIVATOR PROTEIN FOR SPHINGOLIPID HYDROLYSIS IN LIVER AND BRAIN SAMPLES FROM PATIENTS WITH LYSOSOMAL STORAGE DISEASES [J].

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JOURNAL OF CLINICAL INVESTIGATION, 1983, 72 (05) :1622-1628

[9] PROPERTIES OF A PROTEIN ACTIVATOR OF GLYCOSPHINGOLIPID HYDROLYSIS ISOLATED FROM THE LIVER OF A PATIENT WITH GM1 GANGLIOSIDOSIS, TYPE-1 [J].

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[10] THE COHYDROLASES IN HUMAN SPLEEN THAT STIMULATE GLUCOSYL CERAMIDE BETA-GLUCOSIDASE [J].

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