BILIRUBIN AND PARANITROPHENOL GLUCURONYL TRANSFERASE ACTIVITIES OF LIVER IN PATIENTS WITH GILBERTS SYNDROME - ATTEMPT AT A BIOCHEMICAL BREAKDOWN OF GILBERTS SYNDROME

被引:24
作者
AUCLAIR, C
HAKIM, J
BOIVIN, P
TROUBE, H
BOUCHEROT, J
机构
[1] HOP BEAUJON,INSERM 24,RECH UNITE,F-92110 CLICHY,FRANCE
[2] UNIV CLAUDE BERNARD,CTR RECH ENZYMOPATHIES,PARIS,FRANCE
[3] FAC BICHAT BEAUJON,INSERM 24,RECH UNIT,PARIS,FRANCE
关键词
D O I
10.1159/000458848
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:97 / 107
页数:11
相关论文
共 40 条
[2]   CHRONIC NONHEMOLYTIC UNCONJUGATED HYPERBILIRUBINEMIA WITH GLUCURONYL TRANSFERASE DEFICIENCY - CLINICAL, BIOCHEMICAL, PHARMACOLOGIC AND GENETIC EVIDENCE FOR HETEROGENEITY [J].
ARIAS, IM ;
GARTNER, LM ;
COHEN, M ;
EZZER, JB ;
LEVI, AJ .
AMERICAN JOURNAL OF MEDICINE, 1969, 47 (03) :395-&
[3]  
ARIAS IM, 1972, SEMIN HEMATOL, V9, P55
[4]   BILIRUBIN GLUCURONIDE FORMATION INVITRO - DEMONSTRATION OF A DEFECT IN GILBERTS DISEASE [J].
ARIAS, IM ;
LONDON, IM .
SCIENCE, 1957, 126 (3273) :563-564
[5]   BILIRUBIN TURNOVER STUDIES IN NORMAL AND PATHOLOGIC STATES USING BILIRUBIN-14C [J].
BARRETT, PVD ;
BERK, PD ;
MENKEN, M ;
BERLIN, NI .
ANNALS OF INTERNAL MEDICINE, 1968, 68 (02) :355-+
[6]   CONSTITUTIONAL HEPATIC DYSFUNCTION (GILBERTS SYNDROME) - A NEW DEFINITION BASED ON KINETIC STUDIES WITH UNCONJUGATED RADIOBILIRUBIN [J].
BERK, PD ;
BLOOMER, JR ;
HOWE, RB ;
BERLIN, NI .
AMERICAN JOURNAL OF MEDICINE, 1970, 49 (03) :296-&
[7]  
BILLING BH, 1964, CLIN SCI, V27, P245
[8]   HEPATIC BILIRUBIN UDP-GLUCURONYL TRANSFERASE ACTIVITY IN LIVER DISEASE AND GILBERTS SYNDROME [J].
BLACK, M ;
BILLING, BH .
NEW ENGLAND JOURNAL OF MEDICINE, 1969, 280 (23) :1266-&
[9]  
BLACK M, 1970, LANCET, V1, P1359
[10]  
CONNEY AH, 1967, PHARMACOL REV, V19, P317