NORMAL CHOLESTEROL LEVELS WITH LOVASTATIN (MEVINOLIN) THERAPY IN A CHILD WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA FOLLOWING LIVER-TRANSPLANTATION

被引:38
作者
EAST, C
GRUNDY, SM
BILHEIMER, DW
机构
[1] UNIV TEXAS,HLTH SCI CTR,DEPT INTERNAL MED,5323 HARRY HINES BLVD,DALLAS,TX 75235
[2] UNIV TEXAS,HLTH SCI CTR,CTR HUMAN NUTR,DALLAS,TX 75235
来源
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION | 1986年 / 256卷 / 20期
关键词
D O I
10.1001/jama.256.20.2843
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:2843 / 2848
页数:6
相关论文
共 40 条
[1]   MEVINOLIN - A HIGHLY POTENT COMPETITIVE INHIBITOR OF HYDROXYMETHYLGLUTARYL-COENZYME-A REDUCTASE AND A CHOLESTEROL-LOWERING AGENT [J].
ALBERTS, AW ;
CHEN, J ;
KURON, G ;
HUNT, V ;
HUFF, J ;
HOFFMAN, C ;
ROTHROCK, J ;
LOPEZ, M ;
JOSHUA, H ;
HARRIS, E ;
PATCHETT, A ;
MONAGHAN, R ;
CURRIE, S ;
STAPLEY, E ;
ALBERSSCHONBERG, G ;
HENSENS, O ;
HIRSHFIELD, J ;
HOOGSTEEN, K ;
LIESCH, J ;
SPRINGER, J .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (07) :3957-3961
[2]  
ALONSO DR, 1977, AM J PATHOL, V87, P415
[3]  
BEHRMAN RE, 1983, NELSON TXB PEDIATRIC, P1312
[4]  
BERMAN M, 1978, NIH78180 US DHEW PUB
[5]   LIVER-TRANSPLANTATION TO PROVIDE LOW-DENSITY-LIPOPROTEIN RECEPTORS AND LOWER PLASMA-CHOLESTEROL IN A CHILD WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA [J].
BILHEIMER, DW ;
GOLDSTEIN, JL ;
GRUNDY, SM ;
STARZL, TE ;
BROWN, MS .
NEW ENGLAND JOURNAL OF MEDICINE, 1984, 311 (26) :1658-1664
[6]   REDUCTION IN CHOLESTEROL AND LOW-DENSITY LIPOPROTEIN SYNTHESIS AFTER PORTACAVAL-SHUNT SURGERY IN A PATIENT WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA [J].
BILHEIMER, DW ;
GOLDSTEIN, JL ;
GRUNDY, SM ;
BROWN, MS .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 56 (06) :1420-1430
[7]   MEVINOLIN AND COLESTIPOL STIMULATE RECEPTOR-MEDIATED CLEARANCE OF LOW-DENSITY LIPOPROTEIN FROM PLASMA IN FAMILIAL HYPERCHOLESTEROLEMIA HETEROZYGOTES [J].
BILHEIMER, DW ;
GRUNDY, SM ;
BROWN, MS ;
GOLDSTEIN, JL .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (13) :4124-4128
[8]   METABOLIC STUDIES IN FAMILIAL HYPERCHOLESTEROLEMIA - EVIDENCE FOR A GENE-DOSAGE EFFECT INVIVO [J].
BILHEIMER, DW ;
STONE, NJ ;
GRUNDY, SM .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (02) :524-533
[9]   METABOLISM OF VERY LOW-DENSITY LIPOPROTEIN PROTEINS .1. PRELIMINARY IN-VITRO AND IN-VIVO OBSERVATIONS [J].
BILHEIMER, DW ;
LEVY, RI ;
EISENBERG, S .
BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 260 (02) :212-+
[10]  
BONDY PK, 1985, WILLIAMS TXB ENDOCRI, P847