IMPAIRED RECEPTOR-MEDIATED CATABOLISM OF LOW-DENSITY LIPOPROTEIN IN THE WHHL RABBIT, AN ANIMAL-MODEL OF FAMILIAL HYPERCHOLESTEROLEMIA

被引:143
作者
BILHEIMER, DW
WATANABE, Y
KITA, T
机构
[1] UNIV TEXAS,HLTH SCI CTR,DEPT MOLEC GENET,DALLAS,TX 75235
[2] KOBE UNIV,SCH MED,EXPTL ANIM LAB,KOBE 650,JAPAN
来源
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1982年 / 79卷 / 10期
关键词
D O I
10.1073/pnas.79.10.3305
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:3305 / 3309
页数:5
相关论文
共 30 条
[1]  
ATTIE AD, 1981, J BIOL CHEM, V256, P9789
[2]  
Berman M, 1979, Prog Biochem Pharmacol, V15, P67
[3]  
BERMAN M, 1974, SIMULATION ANAL MODE, pX14
[4]   REDUCTION IN CHOLESTEROL AND LOW-DENSITY LIPOPROTEIN SYNTHESIS AFTER PORTACAVAL-SHUNT SURGERY IN A PATIENT WITH HOMOZYGOUS FAMILIAL HYPERCHOLESTEROLEMIA [J].
BILHEIMER, DW ;
GOLDSTEIN, JL ;
GRUNDY, SM ;
BROWN, MS .
JOURNAL OF CLINICAL INVESTIGATION, 1975, 56 (06) :1420-1430
[5]   METABOLIC STUDIES IN FAMILIAL HYPERCHOLESTEROLEMIA - EVIDENCE FOR A GENE-DOSAGE EFFECT INVIVO [J].
BILHEIMER, DW ;
STONE, NJ ;
GRUNDY, SM .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (02) :524-533
[6]   ATHEROSCLEROSIS - LOW-DENSITY LIPOPROTEIN RECEPTOR HYPOTHESIS [J].
GOLDSTEIN, JL ;
BROWN, MS .
METABOLISM-CLINICAL AND EXPERIMENTAL, 1977, 26 (11) :1257-1275
[7]   LOW-DENSITY LIPOPROTEIN PATHWAY AND ITS RELATION TO ATHEROSCLEROSIS [J].
GOLDSTEIN, JL ;
BROWN, MS .
ANNUAL REVIEW OF BIOCHEMISTRY, 1977, 46 :897-930
[8]   LDL RECEPTOR LOCUS AND THE GENETICS OF FAMILIAL HYPERCHOLESTEROLEMIA [J].
GOLDSTEIN, JL ;
BROWN, MS .
ANNUAL REVIEW OF GENETICS, 1979, 13 :259-289
[9]   DETERMINATION OF FREE AMINO GROUPS IN PROTEINS BY TRINITROBENZENESULFONIC ACID [J].
HABEEB, AFS .
ANALYTICAL BIOCHEMISTRY, 1966, 14 (03) :328-&
[10]  
HALL LL, 1974, LAB ANIM SCI, V24, P79