Procoagulant and anticoagulant properties of coagulation factor V:: Factor V Leiden (APC resistance) causes hypercoagulability by dual mechanisms

被引:25
作者
Dahlbäck, B [1 ]
机构
[1] Univ Lund, Univ Hosp MAS, Dept Clin Chem, S-20502 Malmo, Sweden
来源
JOURNAL OF LABORATORY AND CLINICAL MEDICINE | 1999年 / 133卷 / 05期
关键词
D O I
10.1016/S0022-2143(99)90018-5
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
[No abstract available]
引用
收藏
页码:415 / 422
页数:8
相关论文
共 29 条
[1]   Molecular mechanisms of activated protein C resistance - Properties of factor V isolated from an individual with homozygosity for the Arg(506) to Gin mutation in the factor V gene [J].
Aparicio, C ;
Dahlback, B .
BIOCHEMICAL JOURNAL, 1996, 313 :467-472
[2]   MUTATION IN BLOOD-COAGULATION FACTOR-V ASSOCIATED WITH RESISTANCE TO ACTIVATED PROTEIN-C [J].
BERTINA, RM ;
KOELEMAN, BPC ;
KOSTER, T ;
ROSENDAAL, FR ;
DIRVEN, RJ ;
DERONDE, H ;
VANDERVELDEN, PA ;
REITSMA, PH .
NATURE, 1994, 369 (6475) :64-67
[3]   FAMILIAL THROMBOPHILIA DUE TO A PREVIOUSLY UNRECOGNIZED MECHANISM CHARACTERIZED BY POOR ANTICOAGULANT RESPONSE TO ACTIVATED PROTEIN-C - PREDICTION OF A COFACTOR TO ACTIVATED PROTEIN-C [J].
DAHLBACK, B ;
CARLSSON, M ;
SVENSSON, PJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1993, 90 (03) :1004-1008
[4]   THE PROTEIN-C ANTICOAGULANT SYSTEM - INHERITED DEFECTS AS BASIS FOR VENOUS THROMBOSIS [J].
DAHLBACK, B .
THROMBOSIS RESEARCH, 1995, 77 (01) :1-43
[5]  
Dahlback B, 1997, SEMIN HEMATOL, V34, P217
[6]   INHERITED RESISTANCE TO ACTIVATED PROTEIN-C IS CORRECTED BY ANTICOAGULANT COFACTOR ACTIVITY FOUND TO BE A PROPERTY OF FACTOR-V [J].
DAHLBACK, B ;
HILDEBRAND, B .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1994, 91 (04) :1396-1400
[7]  
DAVIE EW, 1995, THROMB HAEMOSTASIS, V74, P1
[8]   THROMBOMODULIN AS A MODEL OF MOLECULAR MECHANISMS THAT MODULATE PROTEASE SPECIFICITY AND FUNCTION AT THE VESSEL SURFACE [J].
ESMON, CT .
FASEB JOURNAL, 1995, 9 (10) :946-955
[9]   ACTIVATED PROTEIN-C RESISTANCE CAUSED BY ARG506GLN MUTATION IN FACTOR VA [J].
GREENGARD, JS ;
SUN, X ;
XU, X ;
FERNANDEZ, JA ;
GRIFFIN, JH ;
EVATT, B .
LANCET, 1994, 343 (8909) :1361-1362
[10]   ACTIVATED PROTEIN-C RESISTANCE - MOLECULAR MECHANISMS BASED ON STUDIES USING PURIFIED GLN(506)-FACTOR-V [J].
HEEB, MJ ;
KOJIMA, Y ;
GREENGARD, JS ;
GRIFFIN, JH .
BLOOD, 1995, 85 (12) :3405-3411