CELL-FREE TRANSLATION OF HUMAN LYSOSOMAL ALPHA-GLUCOSIDASE - EVIDENCE FOR REDUCED PRECURSOR SYNTHESIS IN AN ADULT PATIENT WITH GLYCOGENOSIS TYPE-II

被引：14

作者：

VANDERHORST, GTJ

HOEFSLOOT, EH

KROOS, MA

REUSER, AJJ

机构：

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1987年 / 910卷 / 02期

关键词：

D O I：

10.1016/0167-4781(87)90064-9

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：123 / 129

页数：7

共 28 条

[1]

ANDERSON DJ, 1983, METHOD ENZYMOL, V96, P111

[2]

AUFFRAY C, 1980, EUR J BIOCHEM, V107, P303

[3] MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN [J].

DAZZO, A ;

HOOGEVEEN, A ;

REUSER, AJJ ;

ROBINSON, D ;

GALJAARD, H .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15) :4535-4539

[4] TRANSPORT AND PROCESSING OF ENDOCYTOSED LYSOSOMAL ALPHA-GLUCOSIDASE IN CULTURED HUMAN-SKIN FIBROBLASTS [J].

ELFERINK, RPJO ;

VANDOORNVANWAKEREN, J ;

HENDRIKS, T ;

STRIJLAND, A ;

TAGER, JM .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1986, 158 (02) :339-344

[5] BIOSYNTHESIS AND INTRACELLULAR-TRANSPORT OF ALPHA-GLUCOSIDASE AND CATHEPSIN-D IN NORMAL AND MUTANT HUMAN-FIBROBLASTS [J].

ELFERINK, RPJO ;

VANDOORNVANWAKEREN, J ;

STRIJLAND, A ;

REUSER, AJJ ;

TAGER, JM .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1985, 153 (01) :55-63

[6] ISOLATION AND CHARACTERIZATION OF A PRECURSOR FORM OF LYSOSOMAL ALPHA-GLUCOSIDASE FROM HUMAN-URINE [J].

ELFERINK, RPJO ;

BROUWERKELDER, EM ;

SURYA, I ;

STRIJLAND, A ;

KROOS, M ;

REUSER, AJJ ;

TAGER, JM .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1984, 139 (03) :489-495

[7]

ERICKSON AH, 1983, METHOD ENZYMOL, V96, P38

[8]

ERICKSON AH, 1985, J BIOL CHEM, V260, P4319

[9]

ERICKSON AH, 1979, J BIOL CHEM, V254, P1771

[10]

HASILIK A, 1980, J BIOL CHEM, V255, P4946

← 1 2 3 →