LINEAR RELATIONSHIP BETWEEN THE R-ENANTIOMERS AND S-ENANTIOMERS OF BETA-AMINOISOBUTYRIC ACID IN HUMAN-URINE

被引:24
作者
VANGENNIP, AH
KAMERLING, JP
DEBREE, PK
WADMAN, SK
机构
[1] UNIV UTRECHT, CHILDRENS HOSP, HET WILHELMINA KINDERZIEKENHUIS, 3512 LK UTRECHT, NETHERLANDS
[2] UNIV UTRECHT, DEPT BIOORGAN CHEM, 3522 AD UTRECHT, NETHERLANDS
[3] CHILDRENS HOSP, HET EMMA KINDERZIEKENHUIS, 1018 HJ AMSTERDAM, NETHERLANDS
关键词
D O I
10.1016/0009-8981(81)90045-0
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:261 / 267
页数:7
相关论文
共 13 条
[1]  
ARMSTRONG MD, 1963, J BIOL CHEM, V238, P1447
[2]   VARIABILITY OF METABOLITE EXCRETION IN PROPIONICACIDEMIA [J].
DURAN, M ;
GOMPERTZ, D ;
BRUINVIS, L ;
KETTING, D ;
WADMAN, SK .
CLINICA CHIMICA ACTA, 1978, 82 (1-2) :93-99
[3]  
GREEN A, 1980, INT S INBORN ERRORS, P25
[4]   GAS-CHROMATOGRAPHIC DETERMINATION OF OPTICAL PURITIES OF AMINO-ACIDS USING N-TRIFLUOROACETYL MENTHYL ESTERS [J].
HASEGAWA, M ;
MATSUBARA, I .
ANALYTICAL BIOCHEMISTRY, 1975, 63 (02) :308-320
[5]   BETA-AMINOISOBUTYRATE-ALPHA-KETOGLUTARATE TRANSAMINASE IN RELATION TO BETA-AMINOISOBUTYRIC ACIDURIA [J].
KAKIMOTO, Y ;
KANAZAWA, A ;
TANIGUCHI, K ;
SANO, I .
BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 156 (02) :374-+
[6]  
KAKIMOTO Y, 1961, J BIOL CHEM, V236, P3283
[7]   DETERMINATION OF CONFIGURATIONS OF LACTIC AND GLYCERIC ACIDS FROM HUMAN-SERUM AND URINE BY CAPILLARY GAS-LIQUID-CHROMATOGRAPHY [J].
KAMERLING, JP ;
GERWIG, GJ ;
VLIEGENTHART, JFG ;
DURAN, M ;
KETTING, D ;
WADMAN, SK .
JOURNAL OF CHROMATOGRAPHY, 1977, 143 (02) :117-123
[8]  
NIELSEN HR, 1972, ACTA PATH MICRO IM A, VA 80, P687
[9]   PROPIONYL-COA CARBOXYLASE DEFICIENCY WITH OVERFLOW OF METABOLITES OF ISOLEUCINE CATABOLISM AT ALL LEVELS [J].
PRZYREMBEL, H ;
BREMER, HJ ;
DURAN, M ;
BRUINVIS, L ;
KETTING, D ;
WADMAN, SK ;
BAUMGARTNER, R ;
IRLE, U ;
BACHMANN, C .
EUROPEAN JOURNAL OF PEDIATRICS, 1979, 130 (01) :1-14
[10]   ABSOLUTE-CONFIGURATION OF BETA-AMINOISOBUTYRIC ACID FORMED BY DEGRADATION OF THYMINE IN MAN [J].
SOLEM, E .
CLINICA CHIMICA ACTA, 1974, 53 (02) :183-190