BIOSYNTHESIS AND MATURATION OF GLUCOCEREBROSIDASE IN GAUCHER FIBROBLASTS

被引：80

作者：

JONSSON, LMV

MURRAY, GJ

SORRELL, SH

STRIJLAND, A

AERTS, JFGM

GINNS, EI

BARRANGER, JA

TAGER, JM

SCHRAM, AW

机构：

[1] UNIV AMSTERDAM,INTERSUBFAC VAKGRP BIOCHEM,BIOCHEM LAB,POB 20151,1000 HD AMSTERDAM,NETHERLANDS

[2] NINCDS,MOLEC GENET LAB,MOLEC & MED GENET SECT,BETHESDA,MD 20205

来源：

EUROPEAN JOURNAL OF BIOCHEMISTRY | 1987年 / 164卷 / 01期

关键词：

D O I：

10.1111/j.1432-1033.1987.tb11008.x

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：171 / 179

页数：9

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[5]

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[6]

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[7] GLUCOCEREBROSIDASE PROCESSING IN NORMAL FIBROBLASTS AND IN FIBROBLASTS FROM PATIENTS WITH TYPE-I, TYPE-II, AND TYPE-III GAUCHER DISEASE [J].

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[8]

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[10]

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