BETA-GLUCOSIDASE ACTIVITIES IN HUMAN TISSUES FINDINGS IN GAUCHERS DISEASE

被引:50
作者
HULTBERG, B
OCKERMAN, PA
机构
关键词
D O I
10.1016/0009-8981(70)90176-2
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
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页码:169 / &
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共 16 条
[1]   BETA-D-GLUCOSIDASES AND RELATED ENZYMIC ACTIVITIES IN PIG KIDNEY [J].
ABRAHAMS, HE ;
ROBINSON, D .
BIOCHEMICAL JOURNAL, 1969, 111 (05) :749-&
[2]   RAT-LIVER LYSOSOMAL BETA-GLUCOSIDASE - A MEMBRANE ENZYME [J].
BECK, C ;
TAPPEL, AL .
BIOCHIMICA ET BIOPHYSICA ACTA, 1968, 151 (01) :159-+
[3]  
BRADY RO, 1967, CLIN CHEM, V13, P565
[4]   DEMONSTRATION OF A DEFICIENCY OF GLUCOCEREBROSIDE-CLEAVING ENZYME IN GAUCHERS DISEASE [J].
BRADY, RO ;
KANFER, JN ;
BRADLEY, RM ;
SHAPIRO, D .
JOURNAL OF CLINICAL INVESTIGATION, 1966, 45 (07) :1112-&
[5]  
GATT S, 1966, 3 P INT S CER SPHING, P261
[6]   PROPERTIES OF 4-METHYLUMBELLIFERYL-BETA-GALACTOSIDASE ACTIVITIES IN HUMAN LIVER [J].
HULTBERG, B ;
OCKERMAN, PA .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1969, 23 (03) :213-&
[8]   METABOLISM OF CEREBROSIDE IN INTESTINAL TRACT OF RAT [J].
NILSSON, A .
BIOCHIMICA ET BIOPHYSICA ACTA, 1969, 187 (01) :113-+
[10]   FRACTIONATION OF 4-METHYLUMBELLIFERYL-BETA-GALACTOSIDASE ACTIVITIES IN LIVER IN GARGOYLISM [J].
OCKERMAN, PA ;
HULTBERG, B .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1968, 22 (03) :199-&