STRUCTURES OF SIALYL-OLIGOSACCHARIDES EXCRETED IN URINE OF A PATIENT WITH MUCOLIPIDOSIS-1

被引：31

作者：

MICHALSKI, JC

STRECKER, G

FOURNET, B

CANTZ, M

SPRANGER, J

机构：

[1] UNIV SCI & TECH LILLE 1,CHIM BIOL LAB,VILLENEUVE DASCO,FRANCE

[2] CNRS LAB 217,VILLENEUVE DASCQ,FRANCE

[3] INST JULES DRIESSENS,INST RECH CANC LILLE,F-59020 LILLE,FRANCE

[4] INSERM,UNITE 124,F-59020 LILLE,FRANCE

[5] UNIV MAINZ,CHILDRENS HOSP,D-6500 MAINZ,FED REP GER

来源：

FEBS LETTERS | 1977年 / 79卷 / 01期

关键词：

D O I：

10.1016/0014-5793(77)80359-1

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：101 / 104

页数：4

共 10 条

[1]

BERARD M, 1968, Pathologia Europaea, V3, P172

[2] MUCOLIPIDOSIS-1 - INCREASED SIALIC-ACID CONTENT AND DEFICIENCY OF ANALPHA-N-ACETYLNEURAMINIDASE IN CULTURED FIBROBLASTS [J].

CANTZ, M ;

GEHLER, J ;

SPRANGER, J .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 74 (02) :732-738

[3]

DURAND P, IN PRESS

[4]

MAROTEAUX P, 1975, 2E S EUR MUC ANV

[5]

MICHALSKI J, IN PRESS

[6]

NEUFELD EF, 1974, PROG MED GENET, V10, P81

[7] LIPOMUCOPOLYSACCHARIDOSIS - A NEW STORAGE DISEASE [J].

SPRANGER, J ;

WIEDEMANN, HR ;

TOLKSDORF, M ;

GRAUCOB, E ;

CAESAR, R .

ZEITSCHRIFT FUR KINDERHEILKUNDE, 1968, 103 (04) :285-+

[8]

SPRANGER J, IN PRESS

[9] STRUCTURE OF 3 MAJOR SIALYL-OLIGOSACCHARIDES EXCRETED IN URINE OF 5 PATIENTS WITH 3 DISTINCT INBORN DISEASES - I CELL DISEASE AND 2 NEW TYPES OF MUCOLIPIDOSIS [J].

STRECKER, G ;

HONDIASSAH, T ;

FOURNET, B ;

SPIK, G ;

MONTREUIL, J ;

MAROTEAUX, P ;

DURAND, P ;

FARRIAUX, JP .

BIOCHIMICA ET BIOPHYSICA ACTA, 1976, 444 (02) :349-358

[10]

STRECKER G, IN PRESS

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